Turner syndrome is a sex chromosome disease with a female clinical phenotype. Most patients are diagnosed in childhood or adolescence because of growth delays, and a small number of patients are diagnosed due to TS-related diseases. Women with Turner syndrome can develop hypertension in childhood and adolescence, and the prevalence of hypertension increases with age. The pathogenesis is unclear and may be multifactorial, similar to essential hypertension. In this review article, we explore possible mechanisms, blood pressure management, and treatment recommendations for hypertension in patients with Turner syndrome.